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BAV and the Brain
Berry Aneurysm
Carrie Mettler, pictured
with Dr. Wouter Schievink,
who successfully clipped
the berry aneurysm
behind her left eye.
BAV, Brain Aneurysm and Other Cerebral Complications
Some individuals and families with BAV have been found
to have not only a weakness in the aorta, but also in the
blood vessels of the head and neck. This weakness may
result in brain aneurysm or dissection. One school of
thought is that the vessels in the head and neck are
formed from the same cells as the aortic valve and aorta,
and therefore share the same abnormal tissue.
Studies have begun in this area.
The inspiration for this paper, published in Neurology in
May 2010, was the discovery of a berry aneurysm behind
the left eye of one of the Bicuspid Aortic Foundation’s
board members, Carrie Mettler. Screening for intracranial
aneurysms in patients with bicuspid aortic valve
Another paper, published in November 2012, addresses
another area of concern in those with BAV: Spontaneous
intracranial hypotension in patients with bicuspid aortic
valve
It is interesting to note that Dr. M.E. Abbott, an authority
on BAV and other forms of congenital heart disease,
decades ago documented the sudden death of a 20 year
old with BAV due to a ruptured brain aneurysm (Atlas of
Congenital Heart Disease, 1938, p. 22, Plate IX, Fig 7c).
As screening and follow up are done on more BAV
families, more information will become available.
Brain Aneurysm
Dr. Wouter Schievink
speaking about BAV and
brain aneurysm at a BAF
Conference.